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KMID : 0363219770150020223
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Korean Journal of Dermatology
1977 Volume.15 No. 2 p.223 ~ p.230
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Pityriasis Rubra Pilaris with Bone Involvement
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金永杓/Kim, Young Pio
田寅淇/李厚炯/Chun, Inn Ki/Lee, Hoo Hyung
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Abstract
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Pityriasis rubra Pilaris is a rare, chronic, mildly inflammatory disease cbaracterized by fine acuminate follicular papules, erytheme, scaling of the skin, and recurrent spontaneous remissions and exacerbations. A 19 years old Korean girl presented the clinical symptoms´ of. generalized Pityriasis rubra pilaris, the diagnosis of which was subsequently confirmed by histopathological examination. While associated systemic diseases were absent, some rather dramatic bone changes were observed. These bone changes, similar to those associated with hypervitaminosis-A, included halux valgus, clawed hands and toes, and bone marrow thinning due to the concentric resorption of metacarpal, metatarsal, and phalangeal bones. These bone changes were suspected to be the result of a chronic low-grade bone infection secondany to multiple skin fissuring. As the patient was orphan, the family history could not be obtained. Chromosome analsis was unremarkable. The patient´s history, clinical features, treatment regimen, and prognosis are presented in the study, along with a review of the literatures.
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KEYWORD
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